Staghorn stone in megapolycalicosis in a child: Still the case for open surgery? Case report

Submitted: 7 March 2020
Accepted: 19 January 2022
Published: 2 February 2022
Abstract views:

Publisher's note
All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.


We here report a rare case of congenital megapolycalicosis in a 14-year-old girl complicated by a 24-mm staghorn stone and numerous calculi at the level of all caliceal groups that had become symptomatic in recent weeks with malaise, hematuria, and urinary tract infection. Among the various therapeutic options, we opted for open surgery. The staghorn stone was removed by pyelotomy, and washout of the caliceal cavities released numerous microcalculi of 1.5−9 mm in size that were then removed. To our knowledge, this is the first case of pediatric megacapolycalicosis complicated by staghorn stone, which presents complex problems for the diagnosis and therapy.

Reyes Lara F, Trejo Castillo W. Bol Med Hosp Infant Mex. Congenital megacalycosis. Bol Med Hosp Infant Mex 1982;39:29-31.

Biewald W, Scigalla P, Duda SH. Megacalycosis in childhood. Z Kinderchir 1988;43:427-9. DOI:

Parlaktafi BS, Erdemir F, Uluocak N. Congenital megacalycosis: A rare renal developmental anomaly. Turk J Med Sci 2004;34:401-3.

Redman JF, Neeb AD. Congenital megacalycosis: A forgotten diagnosis? Urology 2005;65:384-5. DOI:

Gittes RF, TalnerLB. Congenital megacalices versus obstructive hydronephrosis. J Urol 1972;108:833-6. DOI:

Prezioso D, Strazzullo P, Lotti T, et Al. Dietary treatment of urinary risk factors for renal stone formation. A review of CLU Working Group. Arch Ital Urol Androl 2015;87:105-20. DOI:

Puigvert A. Le megacalice. J Urol Nephrol 1964;70:321–36. DOI:

Kalaitzis C, Patris E, Deligeorgiou E, et al. Radiological findings and the clinical importance of megacalycosis. Res Rep Urol 2015;7:153–5. DOI:

Mandell GA, Snyder HM 3rd, Heyman S, et al. Association of congenital megacalycosis and ipsilateral segmental ureter. Pediatr Radiol 1987;17:28–33. DOI:

Lam AH. Familial megacalycosis with autosomal recessive inheritance. Report of 3 affected siblings. Pediatr Radiol 1988;19:28-30. DOI:

Hamrick LC, Burns JR. Congenital megacalices in a black woman. J Urol 1985;134:714-5 DOI:

Cacciaguerra S, Bagnara V, Arena C, et al. Megacalycosis on duplex system upper moiety. Eur J Pediatr Surg 1996;6:42-4. DOI:

Bawri B, Puthenveetil RT, Baruah SJ, et al. Megacalycosis or Puigvert disease, a rare congenital calyceal anomaly: A report of 3 cases. UroToday Int J 2012;5:01. DOI:

Pieretti-Vanmarcke R, Pieretti A, Pieretti RV. Megacalycosis: a rare condition. Pediatr Nephrol 2009;24:1077-9. DOI:

Sallami S, Dahmani A, Rhouma SB, et al. Differential diagnosis and management of megacalyces (Puigvert’s disease): A case report. Uro Today Int J 2011;4:13. DOI:

Vargas B, Lebowitz RL. The coexistence of congenital megacalyces and primary megaureter. Am J Roentgenol 1986;147:313-6. DOI:

Gabutti L, Alerci M, Marone C. Spiral CT angiography for discriminating between megacalyces and intermittent hydronephrosis. Nephrol Dial Transplant 1997;12:1487-9. DOI:

Hill LM, Macpherson T, Romano L et al. Prenatal sonographic findings of fetal megacalycosis. J Ultrasound Med 2002;21:1179-81. DOI:

Pereira Arias JG, Gurtubay Arrieta I, Escobal Tamayo V, et al. Megacalycosis and lithiasis. Arch Esp Urol 1995;48:310-4.

Borofsky MS, J Lingeman J. The role of open and laparoscopic stone surgery in the modern era of endourology. Nat Rev Urol 2015;12:392-400. DOI:

Sultan S, Aba Umer S, Ahmed B, et al. Update on surgical management of pediatric urolithiasis. Front Pediatr 2019;7:252. DOI:

Alivizatos G, Skolarikos A. Is there still a role for open surgery in the management of renal stones? Curr Opin Urol 2006;16:106-11. DOI:

Bhojani N, Lingeman JE. Is there still a need for open/laparoscopic surgery for urinary stones? Clin Pract 2012;9:509–14 DOI:

Marte, A. (2022). Staghorn stone in megapolycalicosis in a child: Still the case for open surgery? Case report. La Pediatria Medica E Chirurgica, 44(1).


Download data is not yet available.