https://doi.org/10.4081/pmc.2023.326

Follow-up study of three cases of congenital microgastria

Vol. 45 No. 2 (2023)
Submitted: 17 July 2023
Accepted: 16 October 2023
Published: 15 December 2023
Microgastria, child, GORD, GERD, gastrointestinal, gastric dissociation, jejunal pouch, long-term
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Authors

Sara Ugolini
sara.ugolini@mft.nhs.uk
https://orcid.org/0000-0001-7150-6082
Department of Cardiothoracic Surgery, Wythenshawe Hospital, Manchester University NHS Foundation Trust, Manchester, United Kingdom.
Chiara Oreglio
https://orcid.org/0000-0003-1655-3454
School of Paediatric Surgery, University of Florence, Italy.
Karl Christian Walsh
Department of Plastic Surgery, Wythenshawe Hospital, Manchester University NHS Foundation Trust, Manchester, United Kingdom.
Antonino Morabito
School of Paediatric Surgery, University of Florence, Italy; Department of Pediatric and Neonatal Surgery, AOU Meyer Children’s Hospital IRCCS, Florence, Italy; Department of Neurosciences, Psychology, Drug Research and Child Health (NEUROFARBA), University of Florence, Italy; School of Health and Society, University of Salford, United Kingdom.

Current knowledge on congenital microgastria is limited due to its extreme rarity, and the paucity of nutritional and quality of life follow-ups. Patients affected by congenital microgastria cases followed at out center were screened, and general and nutritional status were evaluated at follow-up visits through validated questionnaires. Three cases were included: one patient died because of a complex syndromic picture where microgastria was imperatively approached conservatively. The remaining cases underwent Hunt-Lawrence at 2 and 17 months. After 2 years and 27 years postoperatively, both patients are on full oral intake. The 28-yearold patient did not reach a BMI higher than 18. She rated her quality of life as unimpacted, with a Gastrointestinal Quality of Life Index of 111. In the other case, parents reported about their 2-yearold child an Infant Gastrointestinal Symptom Questionnaire of 13, corresponding to “no distress”. Our findings confirm the literature trend supporting the role of early surgery in microgastria to improve outcomes. We presented the nutritional status and quality of life in two cases of congenital microgastria operated according to Hunt-Lawrence at a 2-year and 27-year distance, which is the longest follow-up reported to date.

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How to Cite

Ugolini, S., Oreglio, C., Walsh, K. C., & Morabito, A. (2023). Follow-up study of three cases of congenital microgastria. La Pediatria Medica E Chirurgica, 45(2). https://doi.org/10.4081/pmc.2023.326
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