https://doi.org/10.4081/pmc.2023.326
Follow-up study of three cases of congenital microgastria
Submitted: 17 July 2023
Accepted: 16 October 2023
Published: 15 December 2023
Accepted: 16 October 2023
Abstract Views: 592
PDF: 233
HTML: 3
HTML: 3
Publisher's note
All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
Authors
Current knowledge on congenital microgastria is limited due to its extreme rarity, and the paucity of nutritional and quality of life follow-ups. Patients affected by congenital microgastria cases followed at out center were screened, and general and nutritional status were evaluated at follow-up visits through validated questionnaires. Three cases were included: one patient died because of a complex syndromic picture where microgastria was imperatively approached conservatively. The remaining cases underwent Hunt-Lawrence at 2 and 17 months. After 2 years and 27 years postoperatively, both patients are on full oral intake. The 28-yearold patient did not reach a BMI higher than 18. She rated her quality of life as unimpacted, with a Gastrointestinal Quality of Life Index of 111. In the other case, parents reported about their 2-yearold child an Infant Gastrointestinal Symptom Questionnaire of 13, corresponding to “no distress”. Our findings confirm the literature trend supporting the role of early surgery in microgastria to improve outcomes. We presented the nutritional status and quality of life in two cases of congenital microgastria operated according to Hunt-Lawrence at a 2-year and 27-year distance, which is the longest follow-up reported to date.
Ruczynski LIA, Botden SMBI, Daniels-Scharbatke HE, et al. Treatment of congenital microgastria. Eur J Ped Surg 2021;31:129-34.
DOI: https://doi.org/10.1055/s-0040-1710027
Hoehner JC, Kimura K, Soper RT. Congenital microgastria. J Pediatr Surg 1994;29:1591-3.
DOI: https://doi.org/10.1016/0022-3468(94)90228-3
Velasco AL, Holcomb GW, Templeton JM, et al. Management of congenital microgastria. J Pediatr Surg 1990;25:192-7.
DOI: https://doi.org/10.1016/0022-3468(90)90401-T
Furman MS, Connolly SA, Brown SD, et al. The pediatric stomach — congenital abnormalities. Pediatr Radiol. 2021, 51, 2461–2469.
DOI: https://doi.org/10.1007/s00247-021-05155-z
Jones VS, Cohen RC. An eighteen-year follow-up after surgery for congenital microgastria--case report and review of literature. J Pediatr Surg 2007;42:1957-60.
Dicken BJ, Novotny NM, Breckler FD, et al. Use of the Hunt-Lawrence pouch in congenital microgastria--a report of 2 cases. J Pediatr Surg 2010;45:2238-40.
DOI: https://doi.org/10.1016/j.jpedsurg.2010.07.001
Lall A, Morabito A, Bianchi A. "Total Gastric Dissociation (TGD)" in difficult clinical situations. Eur J Pediatr Surg 2006;16:396-8.
DOI: https://doi.org/10.1055/s-2006-924731
Hattori K, Bvulani B, Numanoglu A, et al. Total Esophageal Gastric Dissociation for the Failed Antireflux Procedure in a Child with Microgastria. European J Pediatr Surg Rep 2016;4:006-009.
DOI: https://doi.org/10.1055/s-0035-1571176
Kunisaki SM, Dakhoub A, Jarboe MD, et al. Gastric dissociation for the treatment of congenital microgastria with paraesophageal hiatal hernia. J Pediatr Surg 2011;46:e1-4.
DOI: https://doi.org/10.1016/j.jpedsurg.2011.02.048
Abdelmohsen SM, Sabra TA. Isolated congenital microgastria. J Pediatr Surg Case Rep 2022;79:102217.
DOI: https://doi.org/10.1016/j.epsc.2022.102217
Menon P, Rao KL, Cutinha HP, et al. Gastric augmentation in isolated congenital microgastria. J Pediatr Surg 2003;38:E4-6.
DOI: https://doi.org/10.1016/S0022-3468(03)00518-9
Waasdorp CE, Rooks V, Sullivan C. Congenital microgastria presenting as stridor. Pediatr Radiol 2003;33:662-3.
DOI: https://doi.org/10.1007/s00247-003-0953-2
Shah SS, Rashid A, Bodamer OA. Congenital microgastria-limb reduction association: A case report and review of the literature. Am J Med Genet A 2020;182:2976-81.
DOI: https://doi.org/10.1002/ajmg.a.61872
Shepherd P, Smeulders N, Coleman AHL, et al. Congenital microgastria: A rare cause of failure to visualise the fetal stomach. Prenat Diagn 2011;31:1010-2.
DOI: https://doi.org/10.1002/pd.2821
Mc Laughlin D, Sue T, Thambipillai SP. DOZ047.102: Previously undescribed association of esophageal atresia, congenital microgastria, and pyloric atresia: a difficult case of ‘pure’ atresia. Dis Esophag 2019;32.
DOI: https://doi.org/10.1093/dote/doz047.102
Riley AW, Trabulsi J, Yao M, et al. Validation of a parent report questionnaire. Clin Pediatr (Phila) 2015;54:1167-74.
DOI: https://doi.org/10.1177/0009922815574075
Huang Y, Zhou Y, Li H, et al. The effects of a partially hydrolyzed formula with low lactose and probiotics on mild gastrointestinal disorders of infants: a single-armed clinical trial. Nutrients 2021;13:3371.
DOI: https://doi.org/10.3390/nu13103371
Bellaiche M, Ludwig T, Arciszewska M, et al. Safety and tolerance of a novel anti-regurgitation formula: a double-blind, randomized, controlled trial. J Pediatr Gastroenterol Nutr 2021;73:579-85.
DOI: https://doi.org/10.1097/MPG.0000000000003289
Eypasch E, Williams JI, Wood-Dauphinee S, et al. Gastrointestinal Quality of Life Index: development, validation and application of a new instrument. Br J Surg 1995;82:216-22.
DOI: https://doi.org/10.1002/bjs.1800820229
Fuchs KH, Musial F, Eypasch E, et al. Gastrointestinal quality of life in gastroesophageal reflux disease: a systematic review. Digestion 2022;103:253-260.
DOI: https://doi.org/10.1159/000524766
Bitik B, Tufan A, Mercan R, et al. AB0635-Gastrointestinal quality of life index (GIQLI) in patients with primary sjÖgren’s syndrome. Ann Rheum Dis 2013;71:675.
DOI: https://doi.org/10.1136/annrheumdis-2012-eular.635
Jones VS, Cohen RC. An eighteen year follow-up after surgery for congenital microgastria--case report and review of literature. J Pediatr Surg 2007;1957-60.
DOI: https://doi.org/10.1016/j.jpedsurg.2007.07.054
Atif QAA, Khan MA, Nadeem F, et al. Health-Related Quality of Life After Laparoscopic Cholecystectomy. Cureus 2022;14:e26739.
DOI: https://doi.org/10.7759/cureus.26739
How to Cite
Ugolini, S., Oreglio, C., Walsh, K. C., & Morabito, A. (2023). Follow-up study of three cases of congenital microgastria. La Pediatria Medica E Chirurgica, 45(2). https://doi.org/10.4081/pmc.2023.326
Copyright (c) 2023 the Author(s)
This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.
PAGEPress has chosen to apply the Creative Commons Attribution NonCommercial 4.0 International License (CC BY-NC 4.0) to all manuscripts to be published.
Similar Articles
- F. Taroni, L. Forzenigo, T. Tondolo, N. Liotto, B. Bracco, E. Garavaglia, F. Garbarino, P. Biondetti, F. Mosca, Intra-abdominal Adiposity In Preterm Infants: An Explorative Study , La Pediatria Medica e Chirurgica: Vol. 34 No. 6 (2012)
- C. De Maio, G. Pomero, A. Delogu, E. Briatore, M. Bertero, P. Gancia, Cutis Marmorata Telangiectatica Congenita in a Preterm Female Newborn: Case Report and Review of the Literature , La Pediatria Medica e Chirurgica: Vol. 36 No. 4 (2014)
- M.G. Scarpa, S. Norbedo, F. Murru, M. Bortul, R. Bussani, J. Schleef, An abdominal asimmetry in a 17 years old girl , La Pediatria Medica e Chirurgica: Vol. 34 No. 6 (2012)
- Massimo Agosti, Francesco Tandoi, Laura Morlacchi, Angela Bossi, Nutritional and metabolic programming during the first thousand days of life , La Pediatria Medica e Chirurgica: Vol. 39 No. 2 (2017)
- Enrica Caponcelli, Milena Meroni, Giulia Brisighelli, Claudia Rendeli, Emanuele Ausili, Piergiorgio Gamba, Antonio Marte, Barbara Daniela Iacobelli, Laura Lombardi, Ernesto Leva, Paola Midrio, Transanal irrigation (TAI) in the paediatric population: Literature review and consensus of an Italian multicentre working group , La Pediatria Medica e Chirurgica: Vol. 43 No. 1 (2021)
- Salvatore Fabio Chiarenza, Cosimo Bleve, Ciro Esposito, Maria Escolino, Fabio Beretta, Maurizio Cheli, Vincenzo Di Benedetto, Maria Grazia Scuderi, Giovanni Casadio, Maurizio Marzaro, Leon Francesco Fascetti, Pietro Bagolan, Claudio Vella, Maria Luisa Conighi, Daniela Codric, Simona Nappo, Paolo Caione, Guidelines of the Italian Society of Videosurgery in Infancy for the minimally invasive treatment of pediatric nephrectomy and partial nephrectomy , La Pediatria Medica e Chirurgica: Vol. 39 No. 3 (2017)
- Sara Uccella, Agnese De Carli, Ida Sirgiovanni, Paola Schiavolin, Giuseppe Damiano, Beatrice Ghirardi, Francesca Maglioli Carpano, Laura Bassi, Silvana Gangi, Odoardo Picciolini, Monica Fumagalli, Fabio Mosca, Survival rate and neurodevelopmental outcome of extremely premature babies: an 8-year experience of an Italian single neonatal tertiary care center , La Pediatria Medica e Chirurgica: Vol. 37 No. 3 (2015)
- Agostino Berio, Giacomo Garlaschi, Giuseppe Mangiante, Attilia Piazzi, Oculo-auriculo-vertebral spectrum with craniosynostosis and osteo-cartilagineous multiple defects: a diffuse chondro-membranous-osteo-dysplasia , La Pediatria Medica e Chirurgica: Vol. 37 No. 3 (2015)
- F. Ciuffini, O. Marijke, A. Lavizzari, B. Ghirardi, S. Musumeci, E. Dusi, M. Colnaghi, F. Mosca, Assessment of pulmonary function in a follow-up of premature infants: our experience , La Pediatria Medica e Chirurgica: Vol. 36 No. 3 (2014)
- F. Ciuffini, C. Pietrasanta, A. Lavizzari, S. Musumeci, C. Gualdi, S. Sortino, M. Colnaghi, F. Mosca, Comparison between two different modes of non-invasive ventilatory support in preterm newborn infants with respiratory distress syndrome mild to moderate: preliminary data , La Pediatria Medica e Chirurgica: Vol. 36 No. 4 (2014)
<< < 1 2 3 4 5 6 7 8 9 10 > >>
You may also start an advanced similarity search for this article.